Disease
Granulomatosis with Polyangiitis
Overview Granulomatosis with polyangiitis (GPA), formerly known as Wegener’s granulomatosis, is a rare autoimmune disorder that primarily affects the respiratory tract, kidneys, and upper airways. It is characterized by the inflammation of blood vessels (vasculitis), granuloma formation, and autoantibody production. GPA is a type of anti-neutrophil cytoplasmic antibody (ANCA)-associated vasculitis, Read more…